Scleroderma in Young Woman Would this Illness Associated with Arrhytmogenic Right Ventricular Cardiomyopathy/ Dysplasia?

Dr. Marcelo García Leal
Dr. Marcelo García Leal

Case presentation

This is a patient admitted in the Hospital das Clínicas de Ribeirão Preto, in the Area of Immunologic Therapy, being evaluated for the chance to undergo a BONE MARROW TRANSPLANT, aiming at a better control of systemic sclerosis.
LAB, 18 years old, white, female, college student, born and coming from Porto Alegre – RS. Brazil. Patient without history of previous morbidity. Three years ago she started with manifestations of Systemic Sclerosis, initially with Raynaud’s phenomenon, calcinosis, skin sclerosis.

She started treatment with methotrexate and prednisone; in the meantime she evolved with an insatisfactory response with ulcers in the finger tips and articular retraction. Six months ago she started with mycophenolate mofetil, and to attempt to improve the symptoms of ulcers in the fingers. Three months ago she started with bosentan. There was no evidence of pulmonary hypertension (PAH).

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Auspicios Institucionales
  • Sociedad Argentina de Cardiología
  • Federación Argentina de Cardiología
  • SIAC
  • Asociación Argentina de Cardiología
  • Latin American Heart Rhythm Society
  • Fundación Barceló - Facultad de Medicina